Intraabdominal lymphangiomyoma in an infant with protein-losing enteropathy and hemihypertrophy
TURKISH JOURNAL OF PEDIATRICS, vol.42, no.4, pp.341-343, 2000 (SCI-Expanded, Scopus, TRDizin)
- Publication Type: Article / Article
- Volume: 42 Issue: 4
- Publication Date: 2000
- Journal Name: TURKISH JOURNAL OF PEDIATRICS
- Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Page Numbers: pp.341-343
- Inonu University Affiliated: No
Abstract
Lymphangiomyoma is an extremely rare tumor occurring exclusively in women of reproductive age. The tumor is characterized by proliferation of immature smooth muscle along the lymphatic vessels of the abdomen, thorax and lung. Although lymphangiomyoma has been reported in a young girl and a girl infant, none has been reported in boys. We report herein a case of lympangiomyoma in a two-year-old boy. The unusual presentation in this patient was that the tumor arose from the small bowel mesentery without any evidence of lung involvement. The tumor was extirpated and lymphangiomyomatosis was confirmed pathologically.