The Surgical Repair of a Hyperimmunoglobulin E Syndrome Associated Ascending Aortic Aneurysm

Battaloglu B., Colak C., Disli O. M. , Akca B. , Erdil N. , Karakurt C.

ANNALS OF THORACIC SURGERY, cilt.103, 2017 (SCI İndekslerine Giren Dergi) identifier identifier identifier


Hyperimmunoglobulin E syndrome (HIES) is an immunodeficiency disorder that manifests itself by affecting more than one system. Arterial aneurysms are among the significant complications associated with HIES. Surgical procedures for patients with such aneurysms are uncommon. In this study, we aim to present the case and surgical repair of a male child who was previously diagnosed with HIES and presented with rapidly expanding ascending aortic aneurysm. (C) 2017 by The Society of Thoracic Surgeons