The commonest and most serious complication of neonatal ovarian cysts is torsion. Ovarian torsion leads to loss of the ovary. We report a case of a torsioned and autoamputated right ovarian cyst presenting as a duplication cyst of the intestine in a newborn. An abdominal cystic mass 4.8 X 3.4 cm in diameter was diagnosed in a 36-week-gestation fetus using antenatal ultrasonography (US). The physical examination revealed a mobile abdominal mass in the right upper quadrant. Postnatal US confirmed a cystic mass in the right upper quadrant. Intraoperatively. the ovarian cyst was autoamputated and it was adhered to the antimesenteric edge of the ileum by a fibrotic band. The right ovary could not be found.